%PDF-1.4 % 12 0 obj <> endobj 72 0 obj <>stream /Artifact <>BDC q 1 i 0 841.89 595.276 -841.89 re 297.645 420.96 m W n .015015 841.89 595.29 -841.89 re W n 1 .1 0 .1 k /GS1 gs .015015 0 595.29 31.48 re f EMC /P <>BDC BT /TT4 1 Tf 46 0 0 46 36.6675 670.0925 Tm 1 .89 0 0 k 0 Tc 0 Tw (The Management)Tj ET EMC /P <>BDC BT 46 0 0 46 412.3941 670.0925 Tm ( )Tj ET EMC /P <>BDC BT 46 0 0 46 425.1744 670.0925 Tm ( )Tj ET EMC /P <>BDC BT 46 0 0 46 36.6675 624.8924 Tm (of Severe Intestinal)Tj ET EMC /P <>BDC BT 46 0 0 46 458.484 625.8926 Tm ( )Tj ET EMC /P <>BDC BT 46 0 0 46 36.6675 581.6927 Tm (Dysmotility)Tj ET EMC /Figure <>BDC Q q 1 i 480.855 791.282 99.247 -87.11 re 284.614 581.693 m W* n 0 841.89 595.276 -841.89 re 297.645 420.96 m W n .015015 841.89 595.29 -841.89 re W n /GS1 gs q 90.236 0 0 87.548 488.367 703.974 cm /Im1 Do Q EMC /Artifact <>BDC Q q 1 i 0 841.89 595.276 -841.89 re 297.645 420.96 m W n .015015 841.89 595.29 -841.89 re W n 1 .89 0 0 k /GS1 gs q 1 0 0 1 298.526 549.444 cm 0 0 m 257.014 0 l 258.58 0 259.849 -1.2693 259.849 -2.835 c 259.849 -110.266 l 259.849 -111.832 258.58 -113.101 257.014 -113.101 c -257.014 -113.101 l -258.58 -113.101 -259.849 -111.832 -259.849 -110.266 c -259.849 -2.835 l -259.849 -1.2693 -258.58 0 -257.014 0 c h f* Q EMC /P <>BDC BT /TT2 1 Tf 11 0 0 11 58.6931 521.6911 Tm 0 0 0 0 k 0 Tc .0521 Tw (Severe chronic bowel dysmotility occurs when there is a failure to propel the gut luminal contents)Tj ET EMC /P <>BDC BT 11 0 0 11 538.0776 521.6911 Tm 0 Tw ( )Tj ET EMC /P <>BDC BT 11 0 0 11 58.6931 505.6911 Tm -.0015 Tc -.0402 Tw [(without there being an organic obstructing lesion and the patient is malnourished. )18(The diagnosis can)]TJ ET EMC /P <>BDC BT 11 0 0 11 538.076 505.6911 Tm 0 Tc 0 Tw ( )Tj ET EMC /P <>BDC BT 11 0 0 11 58.6931 489.6911 Tm -.001 Tc -.0407 Tw [(be dif)18(ficult to make, often due to other contributing factors \(e.g. opioids/cyclizine, abdominal surgery)74.2(,)]TJ ET EMC /P <>BDC BT 11 0 0 11 538.0774 489.6911 Tm 0 Tc 0 Tw ( )Tj ET EMC /P <>BDC BT 11 0 0 11 58.6931 473.6911 Tm -.0036 Tc -.0381 Tw [(psychosocial problems and malnutrition\) which themselves can cause/exacerbate dysmotility)74.2(. )18(These)]TJ ET EMC /P <>BDC BT 11 0 0 11 538.0752 473.6911 Tm 0 Tc 0 Tw ( )Tj ET EMC /P <>BDC BT 11 0 0 11 58.6931 457.6911 Tm (patients present with challenging problems requiring a careful multi-disciplinary team \(MDT\) input.)Tj ET EMC /P <>BDC BT /TT4 1 Tf 12 0 0 12 39.993 419.7476 Tm 1 .89 0 0 k (Key points)Tj ET EMC /P <>BDC BT /TT2 1 Tf 8 0 0 8 101.3348 419.7476 Tm 0 0 0 .8 k ( )Tj ET EMC /P <>BDC BT 8 0 0 8 39.993 404.8629 Tm (1.)Tj ET EMC /P <>BDC BT 8 0 0 8 49.109 404.8629 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 404.8629 Tm (Mechanical obstruction must be excluded \(especially if dilated loops)Tj ET EMC /P <>BDC BT 8 0 0 8 291.4606 404.8629 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.109 392.813 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 392.813 Tm [(of bowel are noted\) usually with a CT)18.1( scan of the abdomen after )]TJ ET EMC /P <>BDC BT 8 0 0 8 49.109 380.7629 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 380.7629 Tm (oral contrast. )Tj ET EMC /P <>BDC BT 8 0 0 8 99.7965 380.7629 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 39.993 363.0436 Tm (2.)Tj ET EMC /P <>BDC BT 8 0 0 8 49.109 363.0436 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 363.0436 Tm (Patients with severe chronic small bowel dysmotility may have )Tj ET EMC /P <>BDC BT 8 0 0 8 49.109 350.9936 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 350.9936 Tm [(predominantly a myopathic, a neuropathic or idiopathic aetiology)74.2(. )]TJ ET EMC /P <>BDC BT 8 0 0 8 283.3199 350.9936 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 39.993 333.2743 Tm (3.)Tj ET EMC /P <>BDC BT 8 0 0 8 49.109 333.2743 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 333.2743 Tm [(The patient)18.1(s primary symptoms/problems should be listed in order )]TJ ET EMC /P <>BDC BT 8 0 0 8 49.109 321.2243 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 321.2243 Tm (of importance to the patient and physician)Tj ET EMC /P <>BDC BT 8 0 0 8 199.4254 321.2243 Tm (.)Tj ET EMC /P <>BDC BT 8 0 0 8 201.5681 321.2243 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 39.993 303.5049 Tm (4.)Tj ET EMC /P <>BDC BT 8 0 0 8 49.109 303.5049 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 303.5049 Tm [(Contributing factors \(e.g. drug therapy)74.2(, psychosocial and quality )]TJ ET EMC /P <>BDC BT 8 0 0 8 49.109 291.4551 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 291.4551 Tm (of life issues\) must be evaluated.)Tj ET EMC /P <>BDC BT 8 0 0 8 167.8356 291.4551 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 39.993 273.7358 Tm (5.)Tj ET EMC /P <>BDC BT 8 0 0 8 49.109 273.7358 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 273.7358 Tm [(The patient)18.1(s nutritional status is assessed and, if poor)55.2(, nutritional )]TJ ET EMC /P <>BDC BT 8 0 0 8 49.109 261.6857 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 261.6857 Tm (treatment is begun while taking into account refeeding risks.)Tj ET EMC /P <>BDC BT 8 0 0 8 263.4488 261.6857 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 39.993 243.9665 Tm (6.)Tj ET EMC /P <>BDC BT 8 0 0 8 49.109 243.9665 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 243.9665 Tm (Motility tests to help establish a clinical diagnosis should be )Tj ET EMC /P <>BDC BT 8 0 0 8 49.109 231.9164 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 231.9164 Tm (performed when the patient is not taking any medications that )Tj ET EMC /P <>BDC BT 8 0 0 8 49.109 219.8664 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 219.8664 Tm [(af)18.1(fect gastrointestinal motility \(e.g. opioids and cyclizine\) and ideally )]TJ ET EMC /P <>BDC BT 8 0 0 8 49.109 207.8164 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 207.8164 Tm (when they have achieved a normal body mass index.)Tj ET EMC /P <>BDC BT 8 0 0 8 239.441 207.8164 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 39.993 190.0971 Tm (7.)Tj ET EMC /P <>BDC BT 8 0 0 8 49.109 190.0971 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 190.0971 Tm [(A)55.2( definite diagnosis of dysmotility should not be given unless )]TJ ET EMC /P <>BDC BT 8 0 0 8 49.109 178.0472 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 178.0472 Tm [(it is certain. )18.1(T)110.8(erms such as possible/probable or working diagnosis )]TJ ET EMC /P <>BDC BT 8 0 0 8 49.109 165.9971 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 165.9971 Tm (are )Tj ET EMC /P <>BDC BT 8 0 0 8 65.5049 165.9971 Tm (preferred.)Tj ET EMC /P <>BDC BT 8 0 0 8 100.1885 165.9971 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 39.993 148.2778 Tm (8.)Tj ET EMC /P <>BDC BT 8 0 0 8 49.109 148.2778 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 148.2778 Tm [(A)55.2( plan and treatment goals should be agreed between the patient )]TJ ET EMC /P <>BDC BT 8 0 0 8 49.109 136.2278 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 136.2278 Tm [(and the MDT)18.1( to help symptoms, nutritional status, psycho-social )]TJ ET EMC /P <>BDC BT 8 0 0 8 49.109 124.1778 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 124.1778 Tm [(issues and quality of life. )55.2(All healthcare workers should give the )]TJ ET EMC /P <>BDC BT 8 0 0 8 49.109 112.1278 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 112.1278 Tm (same agreed information to the patient/family/carers. )Tj ET EMC /P <>BDC BT 8 0 0 8 242.5348 112.1278 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 39.993 94.4585 Tm (9.)Tj ET EMC /P <>BDC BT 8 0 0 8 49.109 94.4585 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 94.4585 Tm [(Surgical options may be considered. )18.1(These include insertion )]TJ ET EMC /P <>BDC BT 8 0 0 8 49.109 82.4585 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 82.4585 Tm (of jejunal feeding tubes, venting stomas, a full thickness jejunal )Tj ET EMC /P <>BDC BT 8 0 0 8 49.109 70.4585 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 70.4585 Tm (biopsy and selected bypasses/resections or rarely small bowel )Tj ET EMC /P <>BDC BT 8 0 0 8 49.109 58.4585 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 51.3317 58.4585 Tm (transplantation. )Tj ET EMC /P <>BDC BT 8 0 0 8 108.2574 58.4585 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 305.1843 422.6597 Tm -.1 Tc (10.)Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 422.6597 Tm 0 Tc ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 422.6597 Tm (All injectable treatments should be avoided, particularly cyclizine. )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 410.6597 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 410.6597 Tm (Opioid drugs of all types should also be avoided. If any of these are )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 398.6597 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 398.6597 Tm [(already being used, every ef)18.1(fort should be made to wean the patient)]TJ ET EMC /P <>BDC BT 8 0 0 8 557.4252 398.6597 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 386.6597 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 386.6597 Tm (from them.)Tj ET EMC /P <>BDC BT /TT4 1 Tf 12 0 0 12 354.7533 386.6597 Tm 1 .89 0 0 k ( )Tj ET EMC /P <>BDC BT 12 0 0 12 305.1843 366.3211 Tm (Explanations)Tj ET EMC /P <>BDC BT /TT2 1 Tf 8 0 0 8 379.8679 366.3211 Tm 0 0 0 .8 k ( )Tj ET EMC /P <>BDC BT 8 0 0 8 305.1843 351.4865 Tm -.005 Tc (1.)Tj ET EMC /P <>BDC BT /TT4 1 Tf 8 0 0 8 314.3402 351.4865 Tm 0 Tc ( )Tj ET EMC /P <>BDC BT /TT2 1 Tf 8 0 0 8 316.5228 351.4865 Tm (Mechanical obstruction may not show on radiological investigations.)Tj ET EMC /P <>BDC BT 8 0 0 8 556.6517 351.4865 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 339.4865 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 339.4865 Tm (If the history fits for this \(sudden onset colicky abdominal pain, )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 327.4865 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 327.4865 Tm (borborygmi, and diarrhoea as it resolves\) then a low fibre diet may )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 315.4865 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 315.4865 Tm (be tried. )Tj ET EMC /P <>BDC BT 8 0 0 8 347.6517 315.4865 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 305.1843 297.8173 Tm (2.)Tj ET EMC /P <>BDC BT /TT4 1 Tf 8 0 0 8 314.3002 297.8173 Tm ( )Tj ET EMC /P <>BDC BT /TT2 1 Tf 8 0 0 8 316.5228 297.8173 Tm (Patients with a predominant myopathy have a poorly contracting, )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 285.8173 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 285.8173 Tm [(often dilated gut with bacterial overgrowth. )18.1(This may be referred )]TJ ET EMC /P <>BDC BT 8 0 0 8 314.3002 273.8173 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 273.8173 Tm [(to as chronic intestinal pseudo-obstruction \(CIPO\). )55.2(A)55.2( myopathy )]TJ ET EMC /P <>BDC BT 8 0 0 8 314.3002 261.8173 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 261.8173 Tm (may be due to a primary gut disease \(e.g. hollow visceral )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 249.8172 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 249.8172 Tm (myopathy\) or a secondary disease \(e.g. systemic sclerosis, )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 237.8172 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 237.8172 Tm (dermatomyositis, myotonia dystrophia, amyloid, irradiation )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 225.8172 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 225.8172 Tm (or muscular dystrophies\). )Tj ET EMC /P <>BDC BT 8 0 0 8 408.554 225.8172 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 208.1479 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 208.1479 Tm (An enteric neuropathy is the most common type of enteric )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 196.1479 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 196.1479 Tm (dysmotility and the gut is usually not dilated \(non-CIPO\) and )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 184.1479 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 184.1479 Tm (may constantly contract in an uncoordinated fashion. It is often )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 172.1479 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 172.1479 Tm (secondary to an underlying neurological process that involves the )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 160.1479 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 160.1479 Tm (central and/or peripheral nervous system \(e.g. cerebral, brain stem )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 148.1479 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 148.1479 Tm [(or spinal cord lesion, Parkinson)18.1(s disease, Guillen-Barre syndrome )]TJ ET EMC /P <>BDC BT 8 0 0 8 314.3002 136.1479 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 136.1479 Tm [(or multiple sclerosis\). )55.2(An enteric neuropathy may result from )]TJ ET EMC /P <>BDC BT 8 0 0 8 314.3402 124.1479 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 124.1479 Tm -.005 Tc (autonomic failure \(e.g. diabetes mellitus\) or it can be a paraneoplasic)Tj ET EMC /P <>BDC BT 8 0 0 8 557.8173 124.1479 Tm 0 Tc ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 112.1479 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 112.1479 Tm [(condition \(e.g. from small cell carcinoma of the lung\). More rarely)74.2(, )]TJ ET EMC /P <>BDC BT 8 0 0 8 314.3002 100.1479 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 100.1479 Tm (it is a primary condition \(e.g. a mitochondrial disorder\).)Tj ET EMC /P <>BDC BT 8 0 0 8 509.0463 100.1479 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 82.4785 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 82.4785 Tm (When the pathological process is uncertain the term idiopathic )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 70.4785 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 70.4785 Tm (dysmotility is used. Hypemobile Ehlers-Danlos syndrome fits into )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3002 58.4785 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 316.5228 58.4785 Tm [(this category and is associated with gut hypersensitivity)74.2(.)]TJ ET EMC /P <>BDC BT 8 0 0 8 514.2494 58.4785 Tm ( )Tj ET EMC /P <>BDC BT /TT4 1 Tf 9 0 0 9 22.6772 814.1643 Tm 1 .15 0 0 k [(THE BRITISH INTESTINAL)18.1( F)55.2(AILURE )37.1(ALLIANCE \(BIF)55.2(A\) T)18.1(O)0(P)18.1( TIPS )37.1(ARTICLE SERIES)]TJ ET EMC /Artifact <>BDC 0 0 0 .6 k .015015 806.78 595.29 1.417 re f EMC /P <>BDC BT /TT2 1 Tf 8 0 0 8 22.6772 14.3571 Tm 0 0 0 0 k [(BIF)55.2(A)55.2( is a Specialist Interest Group of ϳԹ )]TJ ET EMC /P <>BDC BT /TT4 1 Tf 8 0 0 8 191.2006 14.3571 Tm [(www)37.1(.bapen.org.uk )]TJ ET EMC /P <>BDC BT /TT2 1 Tf 8 0 0 8 38.993 559.786 Tm 0 0 0 .8 k [(Jeremy Nightingale and the BIF)55.2(A)55.2( Committee)]TJ ET EMC /P <>BDC BT 6 0 0 6 510.4381 41.029 Tm (Continued over page...)Tj ET EMC /P <>BDC BT 8 0 0 8 527.0032 14.3585 Tm 0 0 0 0 k (August 2022)Tj ET EMC Q endstream endobj 73 0 obj <>/XObject<>/ExtGState<>>> endobj 80 0 obj <> endobj 134 0 obj <>stream /Figure <>BDC q 1 i -16 794.836 625.344 -936.03 re 297.645 420.96 m W* n 0 841.89 595.276 -841.89 re 297.645 420.96 m W n .015015 841.89 595.29 -841.89 re W n /GS2 gs q 702.114 106.142 -80.977 535.654 11.868 -89.181 cm /Im2 Do Q EMC /P <>BDC Q q 1 i 0 841.89 595.276 -841.89 re 297.645 420.96 m W n .015015 841.89 595.29 -841.89 re W n /GS1 gs BT /TT4 1 Tf 9 0 0 9 22.6772 814.1656 Tm 1 .15 0 0 k 0 Tc 0 Tw [(THE BRITISH INTESTINAL)18.1( F)55.2(AILURE )37.1(ALLIANCE \(BIF)55.2(A\) T)18.1(O)0(P)18.1( TIPS )37.1(ARTICLE SERIES)]TJ ET EMC /Artifact <>BDC 0 0 0 .6 k .015015 806.781 595.29 1.4171 re f EMC /Artifact <>BDC 1 .1 0 .1 k .015015 0 595.29 31.482 re f EMC /P <>BDC BT /TT2 1 Tf 8 0 0 8 22.6772 14.3583 Tm 0 0 0 0 k [(BIF)55.2(A)55.2( is a Specialist Interest Group of ϳԹ )]TJ ET EMC /P <>BDC BT /TT4 1 Tf 8 0 0 8 191.2007 14.3583 Tm [(www)37.1(.bapen.org.uk )]TJ ET EMC /Artifact <>BDC 0 0 0 .08 k 38 168.632 518.383 175.115 re f EMC /P <>BDC BT 9 0 0 9 55.4701 321.4822 Tm 1 .89 0 0 k (Suggested reading:)Tj ET EMC /P <>BDC BT /TT2 1 Tf 8 0 0 8 163.4701 321.4822 Tm 0 0 0 .8 k ( )Tj ET EMC /P <>BDC BT 8 0 0 8 55.4701 305.6476 Tm ()Tj ET EMC /P <>BDC BT 8 0 0 8 63.974 305.6476 Tm (Camilleri M \(2021\). Gastrointestinal motility disorders in neurologic disease. J Clin Invest.; 131\(4\): e143771. )Tj ET EMC /P <>BDC BT 8 0 0 8 446.8139 305.6476 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 55.4701 292.6476 Tm ()Tj ET EMC /P <>BDC BT 8 0 0 8 63.974 292.6476 Tm [(Kamperidis N, Nightingale J \(2022\). Neurological disorders and small bowel dysmotility)74.2(. Curr Opin Gastroenterol.; 38\(3\): 299-30)]TJ 56.3955 0 TD (6.)Tj ET EMC /P <>BDC BT 8 0 0 8 521.8099 292.6476 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 55.4701 279.6476 Tm ()Tj ET EMC /P <>BDC BT 8 0 0 8 63.974 279.6476 Tm [(Kelly S, Wheatley C and the BIF)55.2(A)55.2( Committee \(2021\). )18.1(T)110.8(op )18.1(T)37.1(ips for managing the psychological well-being of adults requiring home )]TJ ET EMC /P <>BDC BT 8 0 0 8 63.974 266.6476 Tm [(parenteral support \(HPS\). )55.2(Accessed online: www)55.2(.bapen.org.uk/pdfs/bifa/bifa-top-tips-series-13.pdf.)]TJ ET EMC /P <>BDC BT 8 0 0 8 415.267 266.6476 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 55.4701 253.6476 Tm ()Tj ET EMC /P <>BDC BT 8 0 0 8 63.974 253.6476 Tm (Lam C, et al. \(2022\). Gastrointestinal symptoms and nutritional issues in patients with hypermobility disorders: assessment, )Tj ET EMC /P <>BDC BT 8 0 0 8 63.974 240.6476 Tm (diagnosis and management. Frontline Gastroenterol. \(in press\). )Tj ET EMC /P <>BDC BT 8 0 0 8 290.7552 240.6476 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 55.4701 227.6476 Tm ()Tj ET EMC /P <>BDC BT 8 0 0 8 63.974 227.6476 Tm [(Nightingale J, et al. \(2019\). )18.1(The use of cyclizine in patients receiving parenteral nutrition. )55.2(Accessed online: )]TJ ET EMC /P <>BDC BT 8 0 0 8 63.974 214.6476 Tm [(www)55.2(.bapen.org.uk/pdfs/bifa/position-statements/position-statement-on-use-of-cyclizine-in-patients-receiving-pn.pdf.)]TJ ET EMC /P <>BDC BT 8 0 0 8 472.1732 214.6476 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 55.4701 201.6476 Tm ()Tj ET EMC /P <>BDC BT 8 0 0 8 63.974 201.6476 Tm [(Nightingale JMD, et al. \(2020\). )18.1(The management of adult patients with severe chronic small intestinal dysmotility)74.2(. Gut.; 69: 2)]TJ 54.9893 0 TD (074-2092.)Tj ET EMC /P <>BDC BT 8 0 0 8 539.9193 201.6476 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 55.4701 188.6476 Tm ()Tj ET EMC /P <>BDC BT 8 0 0 8 63.974 188.6476 Tm -.015 Tc [(V)74.2(asant DH, Lal S \(2021\). Recent advances in the management of severe gastrointestinal dysmotility)74.2(. Clin Exp Gastroenterol.; 14:)]TJ 55.0867 0 TD ( 163-172. )Tj ET EMC /P <>BDC BT 8 0 0 8 539.4956 188.6476 Tm 0 Tc ( )Tj ET EMC /P <>BDC BT 8 0 0 8 55.4701 176.6476 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 526.4498 14.3583 Tm 0 0 0 0 k (August 2022)Tj ET EMC /P <>BDC BT 8 0 0 8 37.8747 776.0668 Tm 0 0 0 .8 k (3.)Tj ET EMC /P <>BDC BT /TT4 1 Tf 8 0 0 8 46.9906 776.0668 Tm ( )Tj ET EMC /P <>BDC BT /TT2 1 Tf 8 0 0 8 49.2133 776.0668 Tm (The primary symptoms from both an enteric myopathy and )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 764.0668 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 764.0668 Tm (neuropathy are abdominal pain, diarrhoea/constipation, nausea/ )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 752.0668 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 752.0668 Tm [(vomiting bloating and weight loss. )18.1(The abdominal pain often )]TJ ET EMC /P <>BDC BT 8 0 0 8 46.9906 740.0668 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 740.0668 Tm (follows food intake.)Tj ET EMC /P <>BDC BT 8 0 0 8 117.2523 740.0668 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 37.8747 719.5629 Tm (4.)Tj ET EMC /P <>BDC BT /TT4 1 Tf 8 0 0 8 46.9906 719.5629 Tm ( )Tj ET EMC /P <>BDC BT /TT2 1 Tf 8 0 0 8 49.2133 719.5629 Tm [(Many medications may af)18.1(fect gastrointestinal motility)74.2(, especially )]TJ ET EMC /P <>BDC BT 8 0 0 8 46.9906 707.5629 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 707.5629 Tm (opioids which when used chronically can worsen the abdominal )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 695.5629 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 695.5629 Tm (pain \(narcotic bowel syndrome\). Cyclizine in addition to having )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 683.5629 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 683.5629 Tm [(anti-cholinergic ef)18.1(fects appears to be addictive when given as a )]TJ ET EMC /P <>BDC BT 8 0 0 8 46.9906 671.5629 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 671.5629 Tm [(bolus intravenously)74.2(. )]TJ ET EMC /P <>BDC BT 8 0 0 8 121.5492 671.5629 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 651.059 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 651.059 Tm [(Most dysmotility patients have significant psychological morbidity)74.2(, )]TJ ET EMC /P <>BDC BT 8 0 0 8 46.9906 639.059 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 639.059 Tm (which is either primary and precedes the onset of symptoms )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 627.059 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 627.059 Tm (\(e.g. trauma or abuse\), or is closely tied up with the perpetuation )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 615.059 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 615.059 Tm (of symptoms \(or both\). )Tj ET EMC /P <>BDC BT 8 0 0 8 133.682 615.059 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 37.8747 594.555 Tm (5.)Tj ET EMC /P <>BDC BT /TT4 1 Tf 8 0 0 8 46.9906 594.555 Tm ( )Tj ET EMC /P <>BDC BT /TT2 1 Tf 8 0 0 8 49.2133 594.555 Tm (Nutritional treatment starts with preventing/treating refeeding )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 582.555 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 582.555 Tm (problems, then giving oral supplements before considering enteral )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 570.555 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 570.555 Tm (tube feeding \(gastric or jejunal\). Parenteral nutrition is reserved )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 558.555 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 558.555 Tm (for those in whom enteral nutrition fails to maintain or improve )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 546.555 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 546.555 Tm (nutritional status or occasionally in those with pain after any feed )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 534.555 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 534.555 Tm [(\(gastric or jejunal\) and who are also malnourished. )18.1(There is an )]TJ ET EMC /P <>BDC BT 8 0 0 8 46.9906 522.555 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 522.555 Tm (emerging consensus amongst nutrition support teams that )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 510.555 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 510.555 Tm (gastrointestinal dysmotility patients do less well with invasive )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 498.555 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 498.555 Tm (nutrition \(e.g. percutaneous enteral tube feeding, or home )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 486.555 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 486.555 Tm (parenteral support \(HPS\)\). Patients receiving HPS have a )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 474.555 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 474.555 Tm (higher incidence of catheter- related blood stream infections. )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 462.555 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 462.555 Tm [(There should be very careful MDT)18.1( discussion before moving )]TJ ET EMC /P <>BDC BT 8 0 0 8 46.9906 450.555 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 450.555 Tm (towards these treatments, and HPS should be reserved for )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 438.555 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 438.555 Tm (patients who genuinely have intestinal failure. )Tj ET EMC /P <>BDC BT 8 0 0 8 212.4281 438.555 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 37.8747 418.0511 Tm (6.)Tj ET EMC /P <>BDC BT /TT4 1 Tf 8 0 0 8 46.9906 418.0511 Tm ( )Tj ET EMC /P <>BDC BT /TT2 1 Tf 8 0 0 8 49.2133 418.0511 Tm [(T)110.8(ests to establish a diagnosis may include whole gut transit )]TJ ET EMC /P <>BDC BT 8 0 0 8 46.9906 406.0511 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 406.0511 Tm (\(using shapes\), manometry \(though can be poorly tolerated and )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 394.0511 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 394.0511 Tm (availability may be limited\), isotopic gastric emptying/small transit )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 382.0511 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 382.0511 Tm (studies or rarely a full thickness jejunal biopsy \(commonly done )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 370.0511 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 370.0511 Tm (when abdominal surgery is being performed for another reason\). )Tj ET EMC /P <>BDC BT 8 0 0 8 46.9906 358.0511 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 49.2133 358.0511 Tm (Medication \(e.g. opioids, cyclizine or other anticholinergic drugs\) )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 776.0668 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 776.0668 Tm (that may reduce gut transit should be stopped at least 3-5 )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 764.0668 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 764.0668 Tm (days before the tests \(longer if a withdrawal reaction is likely\). )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 752.0668 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 752.0668 Tm (As malnourished patients may have delayed gastric emptying )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 740.0668 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 740.0668 Tm (and gut transit, the nutritional status of the patient should be )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 728.0668 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 728.0668 Tm (as near normal as possible.)Tj ET EMC /P <>BDC BT 8 0 0 8 412.2208 728.0668 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 707.4629 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 707.4629 Tm [(T)110.8(ests to help establish an aetiology include blood tests for )]TJ ET EMC /P <>BDC BT 8 0 0 8 312.17 695.3629 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 695.3629 Tm (hypothyroidism, coeliac disease, diabetes, scleroderma, )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 683.2629 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 683.2629 Tm (paraneoplastic conditions and mitochondrial disorders, and a )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 671.1629 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 671.1629 Tm [(chest X-ray \(or CT/PET)18.1( CT\) for thymoma or other neoplastic )]TJ ET EMC /P <>BDC BT 8 0 0 8 312.17 659.0629 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 659.0629 Tm (conditions \(e.g. small cell carcinoma of the lung\).)Tj ET EMC /P <>BDC BT 8 0 0 8 487.3613 659.0629 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 303.0541 638.4589 Tm (7.)Tj ET EMC /P <>BDC BT /TT4 1 Tf 8 0 0 8 312.17 638.4589 Tm ( )Tj ET EMC /P <>BDC BT /TT2 1 Tf 8 0 0 8 314.3926 638.4589 Tm [(Once a patient is given a diagnosis of dysmotility)74.2(, it is very dif)18.1(ficult )]TJ ET EMC /P <>BDC BT 8 0 0 8 312.17 626.3589 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 626.3589 Tm -.015 Tc (to remove it, hence when not certain \(as is often the case\) a diagnosis)Tj ET EMC /P <>BDC BT 8 0 0 8 554.0098 626.3589 Tm 0 Tc ( )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 614.2589 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 614.2589 Tm [(of possible/probable or a working diagnosis are used. )55.2(As the clinical)]TJ ET EMC /P <>BDC BT 8 0 0 8 554.088 614.2589 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 602.1589 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 602.1589 Tm (situation changes, the diagnosis may be reconsidered or confirmed.)Tj ET EMC /P <>BDC BT 8 0 0 8 554.084 602.1589 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 590.0589 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 590.0589 Tm [(A)55.2( sub-specialist assessment from a neuro-gastroenterologist can )]TJ ET EMC /P <>BDC BT 8 0 0 8 312.17 577.9589 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 577.9589 Tm (be very helpful, although most units have long waiting times, )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 565.8589 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 565.8589 Tm (or restrictions on which patients can be referred.)Tj ET EMC /P <>BDC BT 8 0 0 8 485.1426 565.8589 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 303.0541 545.175 Tm (8.)Tj ET EMC /P <>BDC BT /TT4 1 Tf 8 0 0 8 312.17 545.175 Tm ( )Tj ET EMC /P <>BDC BT /TT2 1 Tf 8 0 0 8 314.3926 545.175 Tm [(There should be an MDT)18.1( that includes psychology and pain )]TJ ET EMC /P <>BDC BT 8 0 0 8 312.17 532.995 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 532.995 Tm (management and it will provide support not only for the patients/)Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 520.815 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 520.815 Tm [(relatives/carers but also for the MDT)110.8(. It is hard to manage these )]TJ ET EMC /P <>BDC BT 8 0 0 8 312.17 508.635 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 508.635 Tm [(patients without a psychological input to the MDT)110.8(. Most patients )]TJ ET EMC /P <>BDC BT 8 0 0 8 312.17 496.455 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 496.455 Tm (will benefit from treatment from a clinical psychologist, although )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 484.275 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 484.275 Tm [(in many hospitals this type of referral can be dif)18.1(ficult to achieve.)]TJ ET EMC /P <>BDC BT 8 0 0 8 538.8068 484.275 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 303.0541 463.5911 Tm (9.)Tj ET EMC /P <>BDC BT /TT4 1 Tf 8 0 0 8 312.17 463.5911 Tm ( )Tj ET EMC /P <>BDC BT /TT2 1 Tf 8 0 0 8 314.3926 463.5911 Tm (In general, surgical procedures are avoided in these patients )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 451.4111 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 451.4111 Tm (for fear of causing adhesions, complications and often not providing )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 439.2311 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 439.2311 Tm (a solution to the symptoms. If abdominal surgery is to be performed,)Tj ET EMC /P <>BDC BT 8 0 0 8 555.3965 439.2311 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 427.0511 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 427.0511 Tm -.01 Tc (a full thickness jejunal biopsy at the same time should be considered.)Tj ET EMC /P <>BDC BT 8 0 0 8 553.8231 427.0511 Tm 0 Tc ( )Tj ET EMC /P <>BDC BT 8 0 0 8 303.0541 406.4471 Tm -.055 Tc (10.)Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 406.4471 Tm 0 Tc (Opioids are no longer used for chronic pain due to the benefits )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 394.3471 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 394.3471 Tm (not being sustained, a risk of causing narcotic bowel syndrome, )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 382.2471 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 382.2471 Tm (and physical and psychological dependence. Intravenous cyclizine )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 370.1471 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 370.1471 Tm (as a bolus is addictive and can damage veins and catheters so )Tj ET EMC /P <>BDC BT 8 0 0 8 312.17 358.0472 Tm ( )Tj ET EMC /P <>BDC BT 8 0 0 8 314.3926 358.0472 Tm (should be avoided. )Tj ET EMC /P <>BDC BT 8 0 0 8 383.7794 358.0472 Tm ( )Tj ET EMC Q endstream endobj 135 0 obj <>/XObject<>/ExtGState<>>> endobj 6 0 obj <> endobj 5 0 obj <> endobj 76 0 obj <>stream Adobed         #"""#''''''''''     !! !!''''''''''""  s!1AQa"q2B#R3b$r%C4Scs5D'6Tdt& EFVU(eufv7GWgw8HXhx)9IYiy*:JZjzm!1AQa"q2#BRbr3$4CS%cs5DT &6E'dtU7()󄔤euFVfvGWgw8HXhx9IYiy*:JZjz?lٳ_ |6lٳf]6lٳdʾJffT OrW!>~KfKy5 xg9(vlٲ?= 8R5/2**3Oag7ռk~{ G8;aœ[, Njۭ{ٳflZ|qmd@i7i6S9?򥞮Q{j%˫D=r[{+IYxËDX@qU{āeٳflV {D6<َ5. )PHLjI 6l̓u Vқc==x& 2FR0p.zw߈ٳbyhM-nJ k@F" q1YkCTЕ-͔TڌKD΋Ywmi40G&$c1!1>)>,Kf͐4/˿=뫲⳧ݾ?ڳ'1I0-)%*6,&=6= 4Sd#ՏJ#C{yٳg"f?2_7"Rhb?PH߮;Gx*1ʁRyi:qBϛ+$kj4(1'3=>} KqF0ŏ+Gf͜cϯi .^s$Svױ_Gr/ ^\yFsi@K>eݒ.[ ~Ԯo?1<48BNO8ni|/<$$(0yu|kM}N,m98,pK̵fݛ6l"Ӽaΐ"Oo=*%u9:ԭ.m3Xt򟔴tNK+{hnڒ?ܻW@.ZyR$GJX+kmU0 9>;.ٳdW-z\F@*+!r ˍZ[@fDK#qݽ:>д3jfK0F$n4h?>fݘ/e4Qii)͎Yj>1O(7~Jٳg>ܾI$bB4}A F37OOd )Q&e*2:0j#<嘴]y5K4 i*Τz7s~L;iŬ'bjOOe}_zqG}=1.!0?f͚͜V)o4l1.,xڒիDGk #Ut]_NճepɺSދOh{ts8I?+\?!jE=CeGN;fiqY|رBczHCiWBٳaG卾^_Ei#F(-Ya]_NSO{S4ٴmZIy-1J4=x{7_tpQtLQf͛f͛<݃f͛6lثf͛6lثf͛6lثf͞ev~QЭ[Xo9/ p^[ IdUMcZҷ&-opIVK[/NG,=O2>Qc5I|Xz~f̀!`H.$O=̏R y-|Ez}R:uytǿpWΧ؍SG4[?f5>hc;˳(rf {6lͺM5Mnj_v2yo]E%{q"D} hHbmG`=[mGq@Ht-pe"Z2Hߺb¼>0(j<+  FqBT+;6lW\ KV+hE9,FuE>sbмOѽ9,ͣı滾.XeZ8E16l(w/~L~lK8r AW \HOjZM3Z|ڗo0*ݽkQ'žX58a)Deg.qvlٳҙkX25@i 5a2X>k78C`H>s]b' 1LL2r6l͛6xCSf͛6lثf͛6lثf͛6lثf͝qi׳;Qaq@P8|dEsӠ62~`灣eH2:XFz_Z͓G\Do7L4fK!N7LD轈]Bٳd[̷;wUBHI#pG|յ7rӢ њ )##z6ڇ"ިᐎ[·8_7I_6ZIw\^xʵ52ZHh{_ct]ri˓Ø 3_vlٲ9K)yMZZ;RC}e:lz:e{3b0|4W47&#j \Nb9)~Y9+SYZ? ?n>s?|I.a+*Zj/O7 ǺǶq=YoDu'&C?N._z\d+qٳf΃47OCg^ w\^ 8;+@~E4Fd[ƆQڈԟB34ũfi<٤FyniFact~J=E-;ы+92GoƧڮĈ_o6.͛66ͩMyuVVZr$i}b9EiEEYEv| -*kխⷚkAKIPRD#! 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